ALDH6A1 Human
目录号 : GP21391Aldehyde Dehydrogenase 6 A1 Human Recombinant
Sample solution is provided at 25 µL, 10mM.
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| Purity | Greater than 85.0% as determined by SDS-PAGE. | Source | Escherichia Coli. |
| Phycical Appearance | Sterile Filtered colorless solution. | Shipping Condition | Shipped with Ice Packs. |
| Synonyms | MMSADHA; MMSDH ; Aldehyde Dehydrogenase 6 Family; MemberA1; Methylmalonate-Semialdehyde Dehydrogenase [Acylating]; Mitochondrial; MitochondrialAcylating Methylmalonate-Semialdehyde Dehydrogenase; Malonate-SemialdehydeDehydrogenase [Acylating]; Aldehyde Dehydrogenase Family 6 Member A1; Malonate-SemialdehydeDehydrogenase; EC 1.2.1.18; EC 1.2.1.27. | ||
| Amino Acid Sequence | MGSSHHHHHHSSGLVPRGSH MGSSSSVPTVKLFIGGKFVE SKSDKWIDIH NPATNEVIGR VPQATKAEMD AAIASCKRAF PAWADTSVLS RQQVLLRYQQLIKENLKEIA KLITLEQGKT LADAEGDVFR GLQVVEHACS VTSLMMGETM PSITKDMDLY SYRLPLGVCAGIAPFNFPAM IPLWMFPMAM VCGNTFLMKP SERVPGATML LAKLLQDSGA PDGTLNIIHG QHEAVNFICDHPDIKAISFV GSNKAGEYIF ERGSRHGKRV QANMGAKNHG VVMPDANKEN TLNQLVGAAF GAAGQRCMALSTAVLVGEAK KWLPELVEHA KNLRVNAGDQ PGADLGPLIT PQAKERVCNL IDSGTKEGAS ILLDGRKIKVKGYENGNFVG PTIISNVKPN MTCYKEEIFG PVLVVLETET LDEAIQIVNN NPYGNGTAIF TTNGATARKY AHLVDVGQVGVNVPIPVPLP MFSFTGSRSS FRGDTNFYGK QGIQFYTQLK TITSQWKEED ATLSSPAVVM PTMGR. | ||
| Stability | Store at 4°C if entire vial will be used within 2-4 weeks. Store, frozen at -20°C for longer periods of time. For long term storage it is recommended to add a carrier protein (0.1% HSA or BSA).Avoid multiple freeze-thaw cycles. | ||
| Formulation | ALDH6A1protein solution (0.25mg/ml) containing Phosphate buffered saline (pH7.4), 10%glycerol and 1mM DTT. | ||
ALDH6A1or Methylmalonate-semialdehydedehydrogenase [acylating], mitochondrial is a mitochondrial methylmalonatesemialdehyde dehydrogenase. ALDH6A1 participates in the valine and pyrimidinecatabolic pathways. ALDH6A1catalyzes the irreversible oxidative decarboxylation of malonate, propionyl-CoAand methylmalonate semialdehydes to acetyl. ALDH6A1 deficiency is distinguishedby high levels of beta-alanine, 3-hydroxypropionic acid, and the two isomers of3-amino and 3-hydroxyisobutyric acids in urine organic acids.
Store at 4°C if entire vial will be used within 2-4 weeks. Store, frozen at -20°C for longer periods of time. For long term storage it is recommended to add a carrier protein (0.1% HSA or BSA).Avoid multiple freeze-thaw cycles.